慢性骨髓单核细胞白血病（Chronic myelomonocytic leukemia，CMML）是一种髓系干细胞疾病，其特点是单核细胞异常增生和积累，并伴有其他骨髓增殖症状。CMML通常会导致脾脏、肝脏、皮肤和淋巴结等器官出现外骨髓表现。然而，耳部表现极为罕见，可能是由于白血病细胞直接浸润、耳蜗、迷路出血、白血病细胞滞留或感染引起的。目前慢性骨髓单核细胞白血病患者的感音神经性听力损失尚没有标准的治疗方案。需要进行更多的研究以改善对该病病因的理解，以提供更好的治疗选择。© 2023. 该作者或作者独家许可给德国施普林格自然出版集团下属公司。

Chronic myelomonocytic leukemia is a myeloid stem cell disease characterized by an abnormal production and accumulation of monocytic cells in association with other signs of myeloproliferation. Extramedullary manifestations of CMML are common and can affect the spleen, liver skin, and lymph nodes. However, otologic manifestations are extremely rare and could have occurred from either direct leukemic infiltration, hemorrhage of the cochlea, labyrinth, leukostasis, or infection. There is no standard treatment protocol for sensorineural hearing loss in CMML patients. More research is needed to improve the understanding of the pathogenesis of this condition, in order to provide better treatment options.© 2023. The Author(s), under exclusive licence to Springer-Verlag GmbH Germany, part of Springer Nature.