肿瘤样原发性中枢神经系统血管炎累及脊柱1例报告
[Tumor-Like Primary Central Nervous System Vasculitis With Spina Involvement:Report of One Case].
发表日期：2024 Jun
作者：
Li Zhang, Hui Sun, Shi-Min Zhang, Sai Gao, Lei Wu, De-Hui Huang
来源：
Brain Structure & Function
摘要：
原发性中枢神经系统血管炎 (PACNS) 是一种主要影响中枢神经系统中小血管的血管炎疾病，累及大脑、脊髓和脑膜。肿瘤样 PNCAS 是 PACNS 的一种罕见亚型，通常在误诊为颅内恶性肿瘤，而脊髓受累的则更为少见。由于缺乏特异性的临床症状和影像学表现，给PACNS的诊断带来了挑战。本报告基于1例肿瘤样脊髓受累的PACNS一例病理证据，旨在丰富对该病的认识。
Primary central nervous system vasculitis (PACNS) is a vasculitic disorder affecting small to medium-sized blood vessels primarily in the central nervous system,involving the brain,spinal cord,and meninges.Tumor-like PNCAS,a rare subtype of PACNS,is often misdiagnosed as intracranial malignancy,and that with spinal cord involvement is even more uncommon.The lack of specific clinical symptoms and imaging manifestations poses a challenge to the diagnosis of PACNS.This report presents a case of tumor-like PACNS with spinal cord involvement based on the pathological evidence,aiming to enrich the knowledge about this condition.