血管错构瘤是由基质细胞和毛细血管细胞组成的良性血管新生物。根据世界卫生组织提出的神经系统肿瘤分类，血管错构瘤被归类为不明原因的一级脑膜瘤。这种肿瘤几乎只发生在中枢神经系统(CNS)中，占所有原发CNS肿瘤的0.9%至2.1%。 在这项描绘性回顾性研究中，伊朗德黑兰城市Shohada-e-Tajrish医院的病理报告档案被回顾，并鉴定出2004-2014年间通过组织病理学检查明确诊断为血管错构瘤的患者。年龄、性别和肿瘤位置从病历中提取，并输入到SPSS统计软件v.22中进行分析。 识别出了30名患者，其中16名为男性(53.3%)，14名为女性(46.7%)。患者的平均年龄为41.2±13.47岁，年龄在19岁至62岁之间。大多数病变发生在患者的小脑(93.3%)，只有一个发生在大脑(3.3%)，另一个发生在第四脑室(3.3%)。 小脑是CNS血管错构瘤患者最常受影响的部位，男性在这些病例中占优势。

Hemangioblastoma refers to a benign vascular neoplasm that comprises stromal and capillary cells. Based on the classification of nervous system tumors proposed by WHO, hemangioblastomas are classified as Grade I meningeal tumors of uncertain origin. These tumors are found almost exclusively in the central nervous system (CNS) and account for 0.9% to 2.1% of all primary CNS tumors.In this descriptive retrospective study, the archives of pathology reports were reviewed in the Department of Pathology of Shohada-e-Tajrish Hospital, Tehran, Iran and patients with definite diagnosis of hemangioblastoma made through histopathological examinations during 2004-2014 were identified. Age, gender and the location of tumor were extracted from the medical records and entered into SPSS statistical software v.22 for analysis.Thirty patients including 16 males (53.3%) and 14 females (46.7%) were identified. The mean age of the patients was calculated to be 41.2±13.47 yr, ranging from 19 to 62 yr old. The majority of lesions had been found in the cerebellum of the patients (93.3%); only one had occurred in the cerebrum (3.3%) and another in the fourth ventricle (3.3%).Cerebellum is the most commonly affected location in patients with CNS hemangioblastomas, and a male preponderance is observed in these cases.