脾和骨上皮样血管内皮瘤：一例报告。
Epithelioid Hemangioendothelioma of Spleen and Bone: A Case Report.
发表日期：2024
作者：
Melvin Denolf, Annelies Rappaport, Sigrun Delvaux
来源：
Bone & Joint Journal
摘要：
上皮样血管内皮瘤（EHE）是一种罕见的血管肿瘤，可起源于各种实质器官、软组织和骨骼。肝外受累极其罕见。在该病例中，脾脏和骨骼中存在多灶性病变。骨病变呈现出目标外观。脾脏病变显示实性成分延迟强化，边缘持续强化。 CAMTA1 染色骨活检证实了诊断。教学要点：当排除其他多灶性疾病时，多灶性骨和脾脏病变的存在可引起 EHE 的怀疑。版权所有：© 2024 作者。
Epithelioid hemangioendothelioma (EHE) is a rare vascular tumor that can originate in various parenchymatous organs, soft tissue, and bone. Extrahepatic involvement is exceedingly rare. In this case, multifocal disease in the spleen and bone was present. Bone lesions showed a target appearance. Splenic lesions showed delayed enhancement of solid components with persistent rim enhancement. A bone biopsy with CAMTA1 staining confirmed the diagnosis. Teaching point: The presence of multifocal bone and splenic lesions can raise suspicion of EHE when other multifocal diseases are excluded.Copyright: © 2024 The Author(s).